怪異村莊：女孩到12歲變成男孩

拉丁美洲有一個與世隔絕的村莊，那里有很多人出生的時候似乎是女孩，但是到12歲時就會變成男孩。這里說的可不是性取向的轉(zhuǎn)變，而是生理構(gòu)造的真實變化。這些特別的孩子會在12歲左右長出陰莖，他們的心理也和正常男孩沒什么兩樣。這種事情在這個村子很常見，當(dāng)?shù)厝艘呀?jīng)見怪不怪了。據(jù)認(rèn)為，這種在青春期性別突變的情況是由于母體子宮內(nèi)缺乏某種酵素導(dǎo)致的，而且已經(jīng)延續(xù)了好幾代人。

In every way, Johnny is physically and biologically male. But, astonishingly he did not grow a penis until he hit puberty.

約翰尼無論在外表上、生理上還是其他各個方面都是一個男孩。但令人驚訝的是，他到了青春期才長出陰莖。

He is one of many children who live in Salinas, an isolated village in the southwestern Dominican Republic, who are seemingly born female, only to become men in their teenage years.

他住在多米尼加共和國西南部偏遠(yuǎn)的薩里那斯村。那里的許多孩子出生時看起來都是女孩，到了青春期才會變成男孩。

Although Johnny’s story may seem extraordinary, cases of little girls turning into boys are so prevalent in the village that it is no longer considered abnormal. The children are simply referred to as the ‘guevedoces’ – which literally translates as ‘penis at 12’.

盡管約翰尼的故事聽起來匪夷所思，但這種女孩變身為男孩的事情在這個村子里卻很常見，人們已經(jīng)見怪不怪了。這些孩子被稱作guevedoce，字面意思翻譯過來就是“12歲的陰莖”。

Johnny, 24, was originally named Felecitia by his parents and brought up as a girl. He spoke to Dr Michael Mosley for the new BBC2 series “Countdown to Life – the extraordinary making of you".

24歲的約翰尼原本被父母取名為費利西提婭，并且被當(dāng)成女孩撫養(yǎng)長大。在英國廣播公司電視2臺拍攝新系列紀(jì)錄片《新生命倒計時——特別的生理構(gòu)造》時，約翰尼與邁克爾•莫斯利博士進(jìn)行了交談。

“I remember I used to wear a little red dress,” he said. “I was born at home instead of in a hospital. They didn’t know what sex I was.

他說：“我記得我以前穿著一條小紅裙。我是在家里出生的，不是在醫(yī)院，所以他們也不知道我的性別。”

“I went to school and I used to wear my skirt. I never liked to dress as a girl. When they bought me girls toys I never bothered playing with them. All I wanted to do was play with the boys.”

“我以前上學(xué)的時候總是穿短裙，但我一直都不喜歡穿成女生的樣子。他們給我買女生的玩具，我都不喜歡玩。我只想跟男生一起玩。”

The rare genetic disorder occurs because of a missing enzyme which prevents the production of a specific form of the male sex hormone - dihydro-testosterone - in the womb.

這種罕見的基因缺陷之所以會發(fā)生，是因為母體子宮內(nèi)缺乏一種酵素，阻止了一種雄性荷爾蒙——雙氫睪酮的產(chǎn)生。

All babies in the womb, whether male or female, have internal glands known as gonads and a small bump between their legs called a tubercle. At around eight weeks, male babies who carry the Y chromosome start to produce dihydro-testosterone in large amounts, which turns the tubercle into a penis. For females, the tubercle becomes a clitoris.

子宮內(nèi)的嬰兒，不管是男是女，體內(nèi)都會有被稱為生殖腺的腺體，雙腿間也會有一處隆起被稱為結(jié)節(jié)。在嬰兒大約八周大的時候，攜帶Y染色體的男嬰兒會大量生產(chǎn)雙氫睪酮，讓結(jié)節(jié)發(fā)育為陰莖，而女嬰兒的結(jié)節(jié)則會變成陰蒂。

But some male babies are missing the enzyme 5-α-reductase which triggers the hormone surge, so they appear to be born female with no testes and what appears to be a vagina. It is not until puberty, when another huge surge of testosterone is produced, that the male reproductive organs emerge. What should have happened in the womb happens around 12 years later. Their voices deepen and they finally grow a penis.

但有一些男嬰兒缺乏促使荷爾蒙大量產(chǎn)生的5α還原酶，所以他們出生時沒有睪丸，只有像陰部一樣的生殖器官，因此，他們被當(dāng)成女孩。只有當(dāng)他們到達(dá)青春期，睪丸激素大量產(chǎn)生時，他們的雄性生殖器官才會出現(xiàn)。這個本該在母體子宮內(nèi)進(jìn)行的過程在12年后才發(fā)生。他們的聲音開始變低沉，并且最終長出了陰莖。

For Johnny it happened at the age of seven. He claimed that he had never felt like a little girl and was far happier after he fully became a boy.

而約翰尼則是在七歲那年長出了陰莖。他說他從來不覺得自己是個女孩，當(dāng)他真正變成男孩的時候，遠(yuǎn)比以前更開心。

“When I changed I was happy with my life,” he said.

他說：“我真正變成男孩以后，對生活十分滿意。”

A little girl named Carla is currently going through the same transformation, aged nine. Despite being brought up as a girl, his mother noticed that from the age of five he was more inclined towards the rough and tumble play of little boys. He has recently had his hair cut short after wearing plaits for years.

一個名叫卡拉的小女孩目前九歲，也在經(jīng)歷同樣的轉(zhuǎn)變階段。盡管他從小就被當(dāng)成女孩撫養(yǎng)長大，他的媽媽早就注意到，他從五歲開始就更喜歡小男孩那些粗魯?shù)目目呐雠龅挠螒颉Ｋ罱舶蚜袅嗽S多年的辮子剪成了短發(fā)。

“I feel like a man now,” he said.

他說：“現(xiàn)在我覺得自己像個男人了。”

Many decide not to change from their female names, so some men in Salinas have names like Catherine.

許多人變成男孩以后決定不改名字，所以薩里那斯村的一些男人會頂著像凱瑟琳之類的女性名字。

Further cases have since been seen in the Sambian villages of Papua New Guinea although the Sambians view the children as flawed males and they are often shunned, unlike the Dominicans who welcome the transformation with widespread celebration.

同樣的事情還發(fā)生在巴布亞新幾內(nèi)亞的塞班村，但是那里的人把這些孩子看作是有缺陷的男性，并且排斥他們，而多米尼加人則很歡迎這種轉(zhuǎn)變，還會舉行大規(guī)模的慶祝活動。

Around one in 90 children in Salinas are guevedoces and although they resemble sexually normal males, subtle differences do still exist in adulthood. Most have decreased amounts of facial hair and smaller prostate glands relative to the average male.

在薩利納斯，每90個孩子就有1個是guevedoce。盡管他們在性別上跟正常男性沒什么兩樣，但成年以后還是會有一些微妙的不同。大多數(shù)人跟一般男性相比，臉上的毛發(fā)更少，前列腺也更小。

It is thought that the condition has persisted through generations because of the isolation of the villagers. Because the disorder is so widespread and accepted, the Dominican Republic now believes that there are three sexual categories, male, female, and pseudohermaphrodite.

由于薩里那斯村村民與外界隔絕，人們認(rèn)為，這種女孩變成男孩的情況已經(jīng)延續(xù)了好幾代人。而由于這種基因缺陷很常見并且已經(jīng)被接受，如今，多米尼加共和國認(rèn)定存在三種性別：男性、女性和假兩性人。